Q85.01 — Neurofibromatosis, type 1
Q85.01

What this code means
Neurofibromatosis type 1 is a genetic condition causing coffee-coloured skin patches and benign nerve tumours (neurofibromas).
Also called: neurofibromatosis type 1, nf1, von recklinghausen disease.
When this code is used
Used for neurofibromatosis, type 1.
Where it sits in ICD-10-CM
Code Q85.01 belongs to Chapter 17: Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders, which covers codes Q00–QA1 in the FY2027 ICD-10-CM tabular list. The official description above is copied verbatim from the CDC/NCHS FY2027 code file.
Related symptoms
Frequently asked questions
What is ICD-10-CM code Q85.01?
Q85.01 is the ICD-10-CM diagnosis code for “Neurofibromatosis, type 1”. Neurofibromatosis type 1 is a genetic condition causing coffee-coloured skin patches and benign nerve tumours (neurofibromas).
When is code Q85.01 used?
Used for neurofibromatosis, type 1. It belongs to Chapter 17 of ICD-10-CM (Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders).
This guide explains ICD-10-CM codes in plain language for patients, students and other readers. It is educational information only — not coding, billing or medical advice. The code recorded for any real encounter is assigned from the full clinical documentation by the treating team and qualified coders, and only they can decide which code fits a specific case.